a.e.g. (1999)

Unified Huntington's Disease Rating Scale (UHDRS) (a.e.g. (2000))

(AAN, 1995)

Nombre:
Varón [ ]
Mujer [ ]
Fecha:
F. nacimiento:
Edad:
Estudios/Profesión:
N. Hª:
Lateralidad:
Fecha del TCE:
Observaciones:

This is a rating system to quantify the severity of Huntington's Disease. It is divided into multiple subsections:motor, cognitive, behavioral, functional. These scores can be calculated by summing the various questions of each section. Some sections (such as chorea and dystonia) require grading each extremity, face, bucco-oral-ligual, and trunk separately. Eye movements require both horizontal and vertical grades.

* Ocular Pursuit (horizontal)

0-complete

1-jerky

2-interrupted/full range

3-incomplete range

4-cannot pursue

* Ocular Pursuit (vertical)

0-complete

1-jerky

2-interrupted/full range

3-incomplete range

4-cannot pursue

* Saccade Initiation (horizontal)

0-normal

1-increased latency

2-suppressible blinks/head movements to

initiate

3-unsuppressible head movements

4-cannot initiate

* Saccade Initiation (vertical)

0-normal

1-increased latency

2-suppressible blinks/head movements to

initiate

3-unsuppressible head movements

4-cannot initiate

* Saccade Velocity (horizontal)

0-normal

1-mild slowing

2-moderate slowing

3-severely slow, full range

4-incomplete range

* Saccade Velocity (vertical)

0-normal

1-mild slowing

2-moderate slowing

3-severely slow, full range

4-incomplete range

* Dysarthria

0-normal

1-unclear, no need to repeat

2-must repeat

3-mostly incomprehensible

4-mute

* Tongue Protrusion

0-normal

1-<10 seconds

2-<5 seconds

3-cannot fully protrude

4-cannot beyond lips

* Finger Taps (right)

0-normal (15/5sec)

1-mild slowing or reduction in amp.

2-moderately impaired. may have occasional

arrests (7- 10/15sec)

3-severely impaired. Frequent hesitations and

arrests

4-can barely perform

* Finger Taps (left)

0-normal (15/5sec)

1-mild slowing or reduction in amp.

2-moderately impaired. may have occasional

arrests (7- 10/15sec)

3-severely impaired. Frequent hesitations and

arrests

4-can barely perform

* Pronate/Supinate (right)

0-normal

1-mild slowing/irregular

2-moderate slowing and irregular

3-severe slowing and irregular

4-cannot perform

* Pronate/Supinate (left)

0-normal

1-mild slowing/irregular

2-moderate slowing and irregular

3-severe slowing and irregular

4-cannot perform

* Fist-Hand-Palm Sequence

0->4 in 10 seconds without cues

1-<4 in 10 sec. without cues

2->4 in 10 sec. with cues

3-<4 in 10 sec. with cues

4-cannot perform

* Rigidity-arms (right)

0-absent

1-slight or only with activation

2-mild/moderate

3-severe, full range of motion

4-severe with limited range

* Rigidity-arms (left)

0-absent

1-slight or only with activation

2-mild/moderate

3-severe, full range of motion

4-severe with limited range

* Bradykinesia

0-normal

1-minimally slow

2-mildly but clearly slow

3-moderately slow

4-marked slowing, long delays in initiation

* Maximal Dystonia(trunk)

0-absent

1-slight/intermittent